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Q85.03

Schwannomatosis

Instruction Source: Q85.03

Schwannomatosis

Instruction Source: Q85.0

Neurofibromatosis (nonmalignant)

Instruction Source: Q85

Phakomatoses, not elsewhere classified

Excludes 1 (Mutually Exclusive)

  • ataxia telangiectasia [Louis-Bar] (G11.3)
  • familial dysautonomia [Riley-Day] (G90.1)
Instruction Source: Q80-Q89

Other congenital malformations (Q80-Q89)

Instruction Source: Q00-QA1

Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders

Excludes 2 (Not Included Here)

  • inborn errors of metabolism (E70-E88)

Clinical Notes

  • Codes from this chapter are not for use on maternal records
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