Ectodermal dysplasia (anhidrotic)

Instruction Source: Q82.4

Ectodermal dysplasia (anhidrotic)

Excludes 1 (Mutually Exclusive)

• Ellis-van Creveld syndrome (Q77.6)

Instruction Source: Q82

Other congenital malformations of skin

Excludes 1 (Mutually Exclusive)

• Sturge-Weber (-Dimitri) syndrome (Q85.89)
• acrodermatitis enteropathica (E83.2)
• congenital erythropoietic porphyria (E80.0)
• pilonidal cyst or sinus (L05.-)

Instruction Source: Q80-Q89

Other congenital malformations (Q80-Q89)

Instruction Source: Q00-QA1

Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders

Excludes 2 (Not Included Here)

• inborn errors of metabolism (E70-E88)

Clinical Notes

• Codes from this chapter are not for use on maternal records