Instruction Source: Q82.2
Congenital cutaneous mastocytosis
Excludes 1 (Mutually Exclusive)
- cutaneous mastocytosis NOS (D47.01)
- diffuse cutaneous mastocytosis (with onset after newborn period) (D47.01)
- malignant mastocytosis (C96.2-)
- systemic mastocytosis (D47.02)
- urticaria pigmentosa (non-congenital) (with onset after newborn period) (D47.01)
Instruction Source: Q82
Other congenital malformations of skin
Excludes 1 (Mutually Exclusive)
- Sturge-Weber (-Dimitri) syndrome (Q85.89)
- acrodermatitis enteropathica (E83.2)
- congenital erythropoietic porphyria (E80.0)
- pilonidal cyst or sinus (L05.-)
Instruction Source: Q80-Q89
Other congenital malformations (Q80-Q89)
Instruction Source: Q00-QA1
Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders
Excludes 2 (Not Included Here)
- inborn errors of metabolism (E70-E88)
Clinical Notes
- Codes from this chapter are not for use on maternal records