Instruction Source: D89.43
Secondary mast cell activation
Instruction Source: D89.4
Mast cell activation syndrome and related disorders
Excludes 1 (Mutually Exclusive)
- (indolent) systemic mastocytosis (D47.02)
- (non-congenital) cutaneous mastocytosis (D47.01)
- aggressive systemic mastocytosis (C96.21)
- congenital cutaneous mastocytosis (Q82.2)
- malignant mast cell neoplasm (C96.2-)
- malignant mastocytoma (C96.29)
- mast cell leukemia (C94.3-)
- mast cell sarcoma (C96.22)
- mastocytoma NOS (D47.09)
- other mast cell neoplasms of uncertain behavior (D47.09)
- systemic mastocytosis associated with a clonal hematologic non-mast cell lineage disease (SM-AHNMD) (D47.02)
Instruction Source: D89
Other disorders involving the immune mechanism, not elsewhere classified
Excludes 1 (Mutually Exclusive)
- hyperglobulinemia NOS (R77.1)
- monoclonal gammopathy (of undetermined significance) (D47.2)
Excludes 2 (Not Included Here)
- transplant failure and rejection (T86.-)
Instruction Source: D80-D89
Certain disorders involving the immune mechanism (D80-D89)
Excludes 1 (Mutually Exclusive)
- autoimmune disease (systemic) NOS (M35.9)
- functional disorders of polymorphonuclear neutrophils (D71-)
Excludes 2 (Not Included Here)
- human immunodeficiency virus [HIV] disease (B20)
Inclusion Terms
- defects in the complement system
- immunodeficiency disorders, except human immunodeficiency virus [HIV] disease
- sarcoidosis
Instruction Source: D50-D89
Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism
Excludes 2 (Not Included Here)
- autoimmune disease (systemic) NOS (M35.9)
- certain conditions originating in the perinatal period (P00-P96)
- complications of pregnancy, childbirth and the puerperium (O00-O9A)
- congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
- endocrine, nutritional and metabolic diseases (E00-E88)
- human immunodeficiency virus [HIV] disease (B20)
- injury, poisoning and certain other consequences of external causes (S00-T88)
- neoplasms (C00-D49)
- symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)