Menu
49 HCC

Specified Lysosomal Storage Disorders

CMS Model V28 13 Associated ICD-10 Diagnoses

Relative Risk Score Factors (Coefficients for HCC 49)

Enrollment Model Type Coeff Tag Year Weight Score
CFA HCC49 2026 + 2.833
CFD HCC49 2026 + 6.399
CNA HCC49 2026 + 9.256
CND HCC49 2026 + 13.778
CPA HCC49 2026 + 3.269
CPD HCC49 2026 + 7.771
INS HCC49 2026 + 1.528

Mapped ICD-10-CM Diagnoses (13)

The following diagnoses map directly to HCC 49 under the V28 risk adjustment model:

ICD-10 Code Clinical Diagnosis Description Guideline
E74.02 Pompe disease Notes ↗
E75.21 Fabry (-Anderson) disease Notes ↗
E75.22 Gaucher disease Notes ↗
E76.01 Hurler's syndrome Notes ↗
E76.02 Hurler-Scheie syndrome Notes ↗
E76.03 Scheie's syndrome Notes ↗
E76.1 Mucopolysaccharidosis, type II Notes ↗
E76.210 Morquio A mucopolysaccharidoses Notes ↗
E76.211 Morquio B mucopolysaccharidoses Notes ↗
E76.219 Morquio mucopolysaccharidoses, unspecified Notes ↗
E76.22 Sanfilippo mucopolysaccharidoses Notes ↗
E76.29 Other mucopolysaccharidoses Notes ↗
E76.3 Mucopolysaccharidosis, unspecified Notes ↗
← Back to V28 Categories Directory