J43.0 Unilateral pulmonary emphysema [MacLeod's syndrome]

Instructional Notes:

J43.0
Description: Unilateral pulmonary emphysema [MacLeod's syndrome]
Inclusion Term:
- Swyer-James syndrome
- Unilateral emphysema
- Unilateral hyperlucent lung
- Unilateral pulmonary artery functional hypoplasia
- Unilateral transparency of lung
↓
J43
Description: Emphysema
Exclude1:
- compensatory emphysema (J98.3)
- emphysema due to inhalation of chemicals, gases, fumes or vapors (J68.4)
- interstitial emphysema (J98.2)
- mediastinal emphysema (J98.2)
- neonatal interstitial emphysema (P25.0)
- surgical (subcutaneous) emphysema (T81.82)
Exclude2:
- emphysema with chronic (obstructive) bronchitis (J44.-)
- emphysematous (obstructive) bronchitis (J44.-)
- traumatic subcutaneous emphysema (T79.7)
↓
J40-J4A
Description: Chronic lower respiratory diseases (J40-J4A)
Exclude1:
- bronchitis due to chemicals, gases, fumes and vapors (J68.0)
Exclude2:
- cystic fibrosis (E84.-)
↓
J00-J99
Description: Diseases of the respiratory system
Exclude2:
- certain conditions originating in the perinatal period (P04-P96)
- certain infectious and parasitic diseases (A00-B99)
- complications of pregnancy, childbirth and the puerperium (O00-O9A)
- congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
- endocrine, nutritional and metabolic diseases (E00-E88)
- injury, poisoning and certain other consequences of external causes (S00-T88)
- neoplasms (C00-D49)
- smoke inhalation (T59.81-)
- symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
Notes:
- When a respiratory condition is described as occurring in more than one site and is not specifically indexed, it should be classified to the lower anatomic site (e.g. tracheobronchitis to bronchitis in J40).
Use Additional Code:
- code, where applicable, to identify:
- exposure to environmental tobacco smoke (Z77.22)
- exposure to tobacco smoke in the perinatal period (P96.81)
- history of tobacco dependence (Z87.891)
- occupational exposure to environmental tobacco smoke (Z57.31)
- tobacco dependence (F17.-)
- tobacco use (Z72.0)