D81.5 Purine nucleoside phosphorylase [PNP] deficiency
Instructional Notes:
-
D81.5
Description: Purine nucleoside phosphorylase [PNP] deficiency
↓
-
D81
Description: Combined immunodeficiencies
Exclude1:
- autosomal recessive agammaglobulinemia (Swiss type) (D80.0)
↓
-
D80-D89
Description: Certain disorders involving the immune mechanism (D80-D89)
Exclude1:
- autoimmune disease (systemic) NOS (M35.9)
- functional disorders of polymorphonuclear neutrophils (D71)
- human immunodeficiency virus [HIV] disease (B20)
Include:
- defects in the complement system
- immunodeficiency disorders, except human immunodeficiency virus [HIV] disease
- sarcoidosis
↓
-
D50-D89
Description: Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism
Exclude2:
- autoimmune disease (systemic) NOS (M35.9)
- certain conditions originating in the perinatal period (P00-P96)
- complications of pregnancy, childbirth and the puerperium (O00-O9A)
- congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
- endocrine, nutritional and metabolic diseases (E00-E88)
- human immunodeficiency virus [HIV] disease (B20)
- injury, poisoning and certain other consequences of external causes (S00-T88)
- neoplasms (C00-D49)
- symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)