D70.0 Congenital agranulocytosis
Instructional Notes:
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D70.0
Description: Congenital agranulocytosis
Inclusion Term:
- Congenital neutropenia
- Infantile genetic agranulocytosis
- Kostmann's disease
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D70
Description: Neutropenia
Exclude1:
- neutropenic splenomegaly (D73.81)
- transient neonatal neutropenia (P61.5)
Use Additional Code:
- code for any associated:
- fever (R50.81)
Include:
- agranulocytosis
- decreased absolute neurophile count (ANC)
Code Also: [', if applicable, mucositis (J34.81, K12.3-, K92.81, N76.81)']
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D70-D77
Description: Other disorders of blood and blood-forming organs (D70-D77)
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D50-D89
Description: Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism
Exclude2:
- autoimmune disease (systemic) NOS (M35.9)
- certain conditions originating in the perinatal period (P00-P96)
- complications of pregnancy, childbirth and the puerperium (O00-O9A)
- congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
- endocrine, nutritional and metabolic diseases (E00-E88)
- human immunodeficiency virus [HIV] disease (B20)
- injury, poisoning and certain other consequences of external causes (S00-T88)
- neoplasms (C00-D49)
- symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)